An unusual case of anti-neutrophilic cytoplasmic autoantibodies associated vasculitis with pauci-immune crescentic glomerulonephritis in young? Wegener’s? Churg Strauss

Authors

  • Bindumathi Pula Lakshmi Department of Internal Medicine, Aster CMI Hospital, Bangalore, Karnataka, India
  • Spandana Peddareddy Department of Internal Medicine, Aster CMI Hospital, Bangalore, Karnataka, India
  • Chethana Dharmapalaiah Department of Rheumatology, Aster CMI Hospital, Bangalore, Karnataka, India
  • Vidyashankar P. Department of Nephrology, Aster CMI Hospital, Bangalore, Karnataka, India
  • Swati Rajagopal Department of Infectious Disease and Travel Medicine, Aster CMI Hospital, Bangalore, Karnataka, India
  • Sunil Kumar K. Department of Interventional Pulmonology, Aster CMI Hospital, Bangalore, Karnataka, India
  • Girish Anand M. S. Department of ENT Surgery, Aster CMI Hospital, Bangalore, Karnataka, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20222541

Keywords:

ANCA-associated vasculitis, Pauci-immune crescentic glomerulonephritis, Corticosteroids, Cyclophosphamide, Rituximab

Abstract

Anti-neutrophilic cytoplasmic autoantibodies-associated vasculitis (AAV) is very rare in India. It normally affects older population around 6th and 7th decade of life. The management of cases is also complicated. We present a case of 18 year old male patient who came with complaints of epistaxis and had hematuria and pain in the joints. He had sub conjunctival haemorrhage on presentation. On and off he had respiratory symptoms and epistaxis in the past for which he was treated as allergy and bronchial asthma. At admission he had high absolute eosinophil count and had blood 3+ positive in urine. Initially he was treated as post viral vasculitis. But patient had involvement of kidney, lung, skin, joints, eyes and on further evaluation he was found to have AAV. The case was unique due to the age of presentation and patient also had overlapping symptoms of both Wegner’s granulomatosis and Churg-Strauss syndrome.

Author Biography

Bindumathi Pula Lakshmi, Department of Internal Medicine, Aster CMI Hospital, Bangalore, Karnataka, India

Deoartment of internal medicine.

Consultant

References

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Published

2022-09-27

How to Cite

Pula Lakshmi, B., Peddareddy, S., Dharmapalaiah, C., P., V., Rajagopal, S., Kumar K., S., & M. S., G. A. (2022). An unusual case of anti-neutrophilic cytoplasmic autoantibodies associated vasculitis with pauci-immune crescentic glomerulonephritis in young? Wegener’s? Churg Strauss. International Journal of Research in Medical Sciences, 10(10), 2307–2311. https://doi.org/10.18203/2320-6012.ijrms20222541

Issue

Section

Case Reports