Cystic nephroma in a 14-year-old-a rare case report
DOI:
https://doi.org/10.18203/2320-6012.ijrms20222966Keywords:
CN, Renal tumour, Case report, HistopathologyAbstract
Cystic nephroma (CN) is an uncommon benign renal tumor with a bimodal age distribution. It often presents with non-specific presenting symptoms. In this study, we report a case of a 14-year-old female patient who presented with a painless abdominal mass, and a left renal cystic lesion was detected on CECT KUB. Left partial nephrectomy was done and a diagnosis of CN made following the histopathological examination of specimen. Owing to its non-specific clinical presentation and radiological findings, it is difficult to distinguish CN from other cystic lesions of kidney like cystic partially differentiated nephroblastoma, tubule-cystic renal cell carcinoma, cystic Wilm’s tumor etc., pre-op. This study emphasizes importance of histopathological examination in diagnosis of CN to prevent misdiagnosis and overtreatment. Although it has good prognosis, long term follow-up for local recurrence is recommended.
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