Intestinal intussusception due to “Rapunzel syndrome” in an adult

Authors

  • Guerrero Gómez Alan Department of General Surgery, Hospital General de Zona 1-A Rodolfo Antonio de la Mucha Macías, IMSS, Mexico City, México
  • López Alvarado Mariela Itzayana Department of General Surgery, Hospital General de Zona 1-A Rodolfo Antonio de la Mucha Macías, IMSS, Mexico City, México https://orcid.org/0000-0001-8709-8917

DOI:

https://doi.org/10.18203/2320-6012.ijrms20230889

Keywords:

Intestinal intussusception, Trichobezoar, Rapunzel syndrome

Abstract

The bezoars are collections of foreign bodies or ingested material that accumulate over time and are often located in the stomach or small intestine,but can be found throughout the digestive tract. Most bezoars are of indigestible organic matter such as trichobezoars (hair); or vegetable and fruit- phytobezoars; or a combination of both but other rare substances have also been described in literature. In some cases, the trichobezoar extends through the pylorus into duodenum, jejunum or even into the colon. Rapunzel syndrome is a rare manifestation of a trichobezoar, which occurs when strands of swallowed hair extend beyond the pylorus of the stomach, into the intestine as a tail. It was first described by Vaughan et al in 1968. Trichobezoars can block the intestinal tract and, if left untreated, can be a life-threatening emergency requiring surgery. Patients are often women, under the age of 20 and have insidious non-specific abdominal symptoms and staggered presentations over months to years. The diagnosis of this type of pathology is usually a challenge for the attending physician, so we present a case report of a 38-year-old female with gastric-intestinal occlusion secondary to trichobezoar.

References

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Published

2023-03-29

How to Cite

Gómez Alan, G., & Mariela Itzayana, L. A. (2023). Intestinal intussusception due to “Rapunzel syndrome” in an adult. International Journal of Research in Medical Sciences, 11(4), 1350–1352. https://doi.org/10.18203/2320-6012.ijrms20230889

Issue

Section

Case Reports