A case of quadriparesis due to renal tubular acidosis accompanied by vitamin D deficiency in Sjögren’s syndrome

Can Hüzmeli, Ferhan Candan, Ersin Tuncer, Meryem Timuçin, Mansur Kayataş


Renal tubular acidosis (RTA) is metabolic acidosis disorder with a normal anion gap that occurs resulting from bicarbonate reabsorption or disorder in the hydrogen excretion from the kidney. A variety of tests are required to be administered in a stepwise fashion for the diagnosis and characterization of RTA. Correct diagnosis involves careful evaluation, including exclusion of other entities causing acidosis. The patients were treated with potassium and bicarbonate supplementation. A fifty-one years old female patient presented to the emergency department with quadriparesis dependent on hypokalemia and vitamin D deficiency, was diagnosed with distal renal tubular acidosis (dRTA) combined with Sjögren's Syndrome (SS). We submitted this case in order to draw attention to the presentation of the RTA with SS.


Sjögren's syndrome, Renal tubular acidosis, Hypokalemia

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