A case report of primary intraabdominal rhabdomyosarcoma presenting as metastasis

Monika Gupta; Nidhi Kaushik; Sujata S. P. Prasad; Sunita Singh

doi:10.18203/2320-6012.ijrms20231369

Authors

Monika Gupta Department of Pathology, PGIMS, Rohtak, Haryana, India
Nidhi Kaushik Department of Pathology, PGIMS, Rohtak, Haryana, India
Sujata S. P. Prasad Department of Pathology, PGIMS, Rohtak, Haryana, India
Sunita Singh Department of Pathology, PGIMS, Rohtak, Haryana, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20231369

Keywords:

Primary, Intestinal,, RMS, Adult

Abstract

Rhabdomyosarcoma (RMS) is a rare and in adult accounts for only 1-3% of all malignant soft tissue tumors. The most frequent sites of origin is within head and neck area. One of the least common sites is the retrorectal-presacral space. This case of 61 years old female is probably the fifth well-documented case of primary abdominopelvic RMS. She presented with abdominal distensions, obstipation, vomiting for 5 days. Excision of the gut wall along with soft tissue mass was done and sent to our department for histopathological examination. On microscopic examination, a diagnosis of malignant mesenchymal tumor with closest resemblance to RMS was made. It is a rare case and needs to bring in notice as there is very few information regarding intraabdominal RMS. This case initially thought to be metastasis from gynecologic malignancy. It is important for pathologists, gynecologists and radiologists to recognize RMS as differential diagnosis of masses arising in abdomen and pelvis.

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