Prostatomegaly in a young adolescent: unusual presentation with rare diagnosis
DOI:
https://doi.org/10.18203/2320-6012.ijrms20232446Keywords:
Prostate, Young age, Ganglion cells, Neurons, Mesenchymal tumourAbstract
Prostatic mesenchymal tumours are extremely uncommon benign tumors and very few cases have been published. Our case presented with diarrhea and increased urinary frequency with normal serum PSA levels. On multi-parametric MRI diffusely enlarging prostate with loss of zonal anatomy with possibility of inflammatory etiology was suggested. Trus guided biopsies were reviewed, which followed by immunohistochemistry aided in the diagnosis of ganglioneuroma. Surgical resection represents the only choice for both diagnosis and treatment. Because of the benign nature of ganglioneuroma, adjuvant chemo or radiotherapy is not indicated but regular follow-up is necessary for an early risk of potential local recurrence. Prostatic ganglioneuroma is the first case being reported to the best of our knowledge. The aim of the study was to document a newly diagnosed entity at this site and segregate more literature about it.
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