Gallbladder agenesis in a patient with choledochoduodenal fistula, report of an exceptional case

Authors

  • Samuel Raul Medina Parra Department of General Surgery, University Hospital of Puebla, BUAP, Mexico
  • Omar Sosa Sánchez Department of General Surgery, University Hospital of Puebla, BUAP, Mexico
  • Rodrígo Migoya Ibarra Department of General Surgery, University Hospital of Puebla, BUAP, Mexico
  • Cheryl Zilahy Díaz Barrientos Department of General Surgery, University Hospital of Puebla, BUAP, Mexico
  • Carlos Alberto Martínez Gandarillas Department of General Surgery, University Hospital of Puebla, BUAP, Mexico
  • José Miguel Espinosa González Department of Endoscopy, University Hospital of Puebla, BUAP, Mexico

DOI:

https://doi.org/10.18203/2320-6012.ijrms20232145

Keywords:

Liver, Agenesis, Gallbladder, Surgery, Leukocytosis

Abstract

Vesicular agenesis refers to the congenital absence of the gallbladder, however, vesicular agenesia is a very scarce condition worldwide, so there is little information available on its clinical presentation and surgical data. This is a 79-year-old male patient, with a history of diabetes mellitus of long evolution, without a surgical history, who comes for colic pain of 15 days of evolution in right hypochondrium, as well as unquantified fever and jaundice, during its initial evaluation in the emergency room para clinics were requested observing leukocytosis, hyperbilirubinemia and elevation of liver enzymes, ultrasound of liver and bile ducts reported common anatomical situation gallbladder, occupied entirely by multiple hyperechogenic images, configuring sign of W.E.S. and common bile duct of 7.2 mm, concluding gallbladder scleroatrophic and vesicular agenesia during trans-surgery. Vesicular agenesis is an extremely rare condition that is mostly diagnosed during surgery, which can lead to erroneous diagnosis and unnecessary surgery in patients with symptoms including biliary colic, choledocholithiasis with or without cholangitis, and an ultrasound showing a scleroatrophic gallbladder. Surgeons In situations where there is clinical evidence consistent with biliary colic in a context of gallbladder agenesis, and the symptoms persist without finding any other cause, a surgical approach to release adhesions could be considered; since, as observed, this may result in improved symptoms, although the explanation is not yet completely clear.

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Published

2023-07-05

How to Cite

Parra, S. R. M., Sánchez, O. S., Ibarra, R. M., Barrientos, C. Z. D., Gandarillas, C. A. M., & González, J. M. E. (2023). Gallbladder agenesis in a patient with choledochoduodenal fistula, report of an exceptional case. International Journal of Research in Medical Sciences, 11(8), 3012–3016. https://doi.org/10.18203/2320-6012.ijrms20232145

Issue

Section

Case Reports