Isolated IgG4-related sclerosing cholangitis mimicking hilar cholangiocarcinoma: a case report of a challenging disease

Dinesh Kumar; Sana Sana; M. Shariq; Nimit Dhabalia

doi:10.18203/2320-6012.ijrms20232816

Authors

Dinesh Kumar Department of Radiology, BHR University Hopsitals NHS Trust, Romford, United Kingdom
Sana Sana Department of Radiology, ABVIMS and Dr. Ram Manohar Lohia Hospital, New Delhi, India
M. Shariq Department of Interventional Radiology, Queen’s Hospital, Romford, United Kingdom
Nimit Dhabalia Department of Radiology, Proscan Diagnostics, Andheri East, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20232816

Keywords:

IgG4-related disease, Sclerosing cholangitis, Cholangiocarcinoma

Abstract

IgG4-related disease (IgG4-RD) has recently attracted attention worldwide; however, its diagnosis still remains challenging. It is an immune-mediated multisystem disease affecting a wide range of organs in the human body. Even though it's uncommon, IgG4-sclerosing cholangitis, which is a biliary manifestation of IgG4-RD, can happen without pancreatic involvement. Here, we report a case of a patient with imaging features typical of hilar cholangiocarcinoma, which eventually turned out to be IgG4 sclerosing cholangitis.

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