A case of concomitant connective tissue disorder and thrombotic thrombocytopenic purpura in an Indian middle aged female

Shubhank Narula; Atul Kakar; Atul Gogia; Tanvi Batra

doi:10.18203/2320-6012.ijrms20233055

Authors

Shubhank Narula Department of Family Medicine, Sir Ganga Ram Hospital, New Delhi, India
Atul Kakar Department of Medicine, Sir Ganga Ram Hospital, New Delhi, India
Atul Gogia Department of Medicine, Sir Ganga Ram Hospital, New Delhi, India
Tanvi Batra Department of Medicine, Sir Ganga Ram Hospital, New Delhi, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20233055

Keywords:

Connective tissue disorder, Seizures, Thrombotic thrombocytopenic purpura, Rituximab

Abstract

Thrombotic thrombocytopenia (TTP) is a rare disease which is rarely present in adults. Adults usually have an acquired version of disease, associated with some underlying autoimmune disease. There has been paucity of literature about reports which shows the coexistence of connective tissue disorder in patients of acquired TTP. This is a case report of a female who presented with vague symptoms of breathlessness, abdominal pain and petechial rashes and was diagnosed as TTP, developed neurological complications but was stabilized by timely management through plasma exchanges and steroids.

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References

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