Non-functioning adrenocortical carcinoma requiring radical nephrectomy-case report with review of literature

Abishek H. Karthik; Bhaskarapprakash A. R.; Radhakrishnan R.; Natarajan B.; Selvaraj V.

doi:10.18203/2320-6012.ijrms20233406

Authors

Abishek H. Karthik Department of Urology, Meenakshi Medical College Hospital and Research Institute, Kanchipuram, Tamil Nadu, India
Bhaskarapprakash A. R. Department of Urology, Meenakshi Medical College Hospital and Research Institute, Kanchipuram, Tamil Nadu, India https://orcid.org/0000-0001-8670-855X
Radhakrishnan R. Department of Urology, Meenakshi Medical College Hospital and Research Institute, Kanchipuram, Tamil Nadu, India
Natarajan B. Department of Urology, Meenakshi Medical College Hospital and Research Institute, Kanchipuram, Tamil Nadu, India
Selvaraj V. Department of Urology, Meenakshi Medical College Hospital and Research Institute, Kanchipuram, Tamil Nadu, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20233406

Keywords:

Non-functional, Adreno-cortical carcinoma, Anaplastic, Aggressive

Abstract

Adrenocortical carcinoma (ACC) is rare malignancy of the adrenal gland and is the second most aggressive endocrine malignant disease after anaplastic thyroid carcinoma. These tumours can be detected very late as majority are non-functional, i.e., does not secrete any hormones, and only present with vague symptoms. Surgical management of such tumours can be challenging as it can invade the surrounding structures making it very difficult for resection. This is a case of a 61-year male with a large non-functioning adrenal tumour which appeared to be separate from the kidney in the radiological imaging but was found stuck to the renal parenchyma posing a dilemma for the operating team.

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