Multiple hamartomatosis of the biliary tract: case report

Abstract

Von Meyenburg complex or multiple biliary hamartomatosis is a rare clinical diagnosis, with a reported prevalence of up to 5.6% in large autopsy series. Since this type of pathology often lacks clinical symptoms, it is usually an incidental finding. We present the case of an 85-year-old female referred to our unit for persistent jaundice, abdominal pain and weight loss. The diagnosis and management of this pathology is often a challenge, the natural history of these cases remains unknown, and neither follow-up nor treatment protocols have been developed in patients with multiple biliary hamartomatosis. Multiple biliary hamartomatosis is a rare pathology which has no specific treatment, however, knowing about it allows a good differential diagnosis with obstructive and parenchymal hepatic pathology.