Arrhythmogenic right ventricular dysplasia: a rare case report from tribal zone of Central India

Authors

  • Prakash Khunte Department of Medicine, Government Medical College, Rajnandgaon, Chhattisgarh
  • Pradeep Beck Department of Medicine, Government Medical College, Rajnandgaon, Chhattisgarh
  • Bajrang Basal Department of Medicine, Pt. J.N.M. Medical College Raipur, Chhattisgarh

Keywords:

ARVD arrhythmogenic right ventricular dysplasia, VT ventricular tachycardia, PSVT paroxysomal supra ventricular tachycardia

Abstract

Arrhythmogenic Right Ventricular Dysplasia (ARVD) is under diagnosed cardiomyopathy which commonly presents in young adults with ventricular tachycardia or sudden death. It is characterized pathologically by progressive fibrofatty replacement of the myocardium, primarily of the right ventricular free wall. Clinically, it presents with life-threatening malignant ventricular arrhythmias which may lead to sudden death, most often in young people and athletes. ARVD/C is difficult to diagnose, although standardized diagnostic criteria have been proposed, based on the presence of major and minor criteria encompassing electrocardiographic, arrhythmic, morphofunctional, histopathologic, and genetic factors.

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Published

2017-01-07

How to Cite

Khunte, P., Beck, P., & Basal, B. (2017). Arrhythmogenic right ventricular dysplasia: a rare case report from tribal zone of Central India. International Journal of Research in Medical Sciences, 3(4), 1025–1029. Retrieved from https://www.msjonline.org/index.php/ijrms/article/view/1435

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Section

Case Reports