A case of Ebstein’s anomaly in an adult female

Anushka Mantina; Srishti Mishra; Spoorthi Ilangovan; Joshmi Vijayakrishnan

doi:10.18203/2320-6012.ijrms20252430

Authors

Anushka Mantina MVJ Medical College and Research Hospital, Hoskote, Bengaluru, Karnataka, India https://orcid.org/0009-0006-5546-0874
Srishti Mishra MVJ Medical College and Research Hospital, Hoskote, Bengaluru, Karnataka, India https://orcid.org/0009-0002-0352-8946
Spoorthi Ilangovan MVJ Medical College and Research Hospital, Hoskote, Bengaluru, Karnataka, India https://orcid.org/0009-0003-7578-1876
Joshmi Vijayakrishnan MVJ Medical College and Research Hospital, Hoskote, Bengaluru, Karnataka, India https://orcid.org/0009-0001-7283-2805

DOI:

https://doi.org/10.18203/2320-6012.ijrms20252430

Keywords:

Ebstein’s anomaly, Cone reconstruction, Adult congenital heart disease, Tricuspid regurgitation

Abstract

Ebstein’s anomaly is a congenital cyanotic heart disease of the tricuspid valve and right ventricle, often diagnosed in childhood but can occasionally be present in adulthood with variable clinical manifestations. Here, we report the case of a 25-year-old female with no prior cardiac history who presented with progressive exertional dyspnoea, palpitations, and intermittent dizziness for a year. Subsequently, the baseline and diagnostic investigations were done and the patient was diagnosed with Ebstein's anomaly with severe tricuspid regurgitation. The patient was started on medical management but due to persistent symptoms surgical correction was done. There was a significant improvement in her symptoms thereafter. Hence this case highlights the importance of considering congenital heart diseases as a cause of heart failure in adults.

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