Arrhythmogenic cardiomyopathy: from concealed phase to refractory failure: a nine-year case study illustrating diagnostic evolution and biventricular progression

Lyudmila Kolochey; Saarah D. Allahudeen; Ibrahim R. R. Haq; Zahra F. Z. Fayik; Udani D. M. Sarathchandra

doi:10.18203/2320-6012.ijrms20261353

Authors

Lyudmila Kolochey Department of Internal Medicine, Grodno State Medical University, Grodno, Belarus
Saarah D. Allahudeen Department of Internal Medicine, Grodno State Medical University, Grodno, Belarus
Ibrahim R. R. Haq Department of Internal Medicine, Grodno State Medical University, Grodno, Belarus
Zahra F. Z. Fayik Department of Internal Medicine, Grodno State Medical University, Grodno, Belarus
Udani D. M. Sarathchandra Department of Internal Medicine, Grodno State Medical University, Grodno, Belarus

DOI:

https://doi.org/10.18203/2320-6012.ijrms20261353

Keywords:

Arrhythmogenic cardiomyopathy, Coronary angiography, Ventricular fibrillation, implantable cardioverter-defibrillator.

Abstract

Arrhythmogenic cardiomyopathy (ACM) is a type of cardiomyopathy characterized by fibrofatty replacement of the right ventricular myocardium and associated with life-threatening arrhythmias. The criteria of the diagnosis of ACM are based on the estimates of structural changes in the right ventricular myocardium, electrocardiographic changes, fibrofatty dystrophy in the course of a histological investigation, and a family history of the disease. The diagnosis can be a challenging task as there are no pathognomonic clinical markers, which makes differential diagnosis of ACM with secondary myocardial pathology more difficult to perform. The article presents a nine-year-old case study of a young male patient with ACM, dominated by life-threatening ventricular arrhythmias and episode of resuscitated sudden cardiac death despite optimal medical therapy and cardioverter-defibrillator implantation.

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