The sprengel deformity

Authors

  • Mohd E. Rasul Department of Radiology, D Y Patil Medical College, Pune, Maharashtra
  • Annu V. Reddy Department of Radiology, D Y Patil Medical College, Pune, Maharashtra

DOI:

https://doi.org/10.18203/2320-6012.ijrms20151457

Keywords:

Birth defects, High scapula, shoulder, Sprengel deformity, Undescended scapula

Abstract

Sprengel shoulder is a rare congenital deformity of one or both scapulae that is usually detected at birth. It occurs due to failure of the scapula to descend during intrauterine development. Although the deformity appears randomly most of the time, familial cases have been reported. Sprengel shoulder is often associated with Klippel-Feil syndrome and other congenital skeletal deformities. Anteroposterior X-ray imaging can accurately diagnose Sprengel deformity. However, computed tomography and magnetic resonance scans with three-dimensional reconstruction are nowadays used in everyday practice in order to diagnose concomitant abnormalities, study in detail the anatomy of the affected shoulder(s), and plan appropriate management. We present here our imaging experience from one pediatric case with Sprengel shoulder and take the opportunity to discuss this rare entity, which is, nevertheless, the commonest congenital defect of the scapula.

References

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Published

2017-01-17

How to Cite

Rasul, M. E., & Reddy, A. V. (2017). The sprengel deformity. International Journal of Research in Medical Sciences, 3(12), 3869–3871. https://doi.org/10.18203/2320-6012.ijrms20151457

Issue

Section

Case Reports