A rare case of mixed connective tissue disease presenting with central nervous system glioma, vasculitis and polymyositis

Authors

  • Rushabh Parikh Department of General Medicine, D Y Patil University School of Medicine, Navi Mumbai
  • Pushkar Ingale Department of General Medicine, D Y Patil University School of Medicine, Navi Mumbai
  • Dhaval Dave Department of General Medicine, D Y Patil University School of Medicine, Navi Mumbai
  • Manish Pendse Department of General Medicine, D Y Patil University School of Medicine, Navi Mumbai
  • Smita Patil Department of General Medicine, D Y Patil University School of Medicine, Navi Mumbai
  • Archana Bhate Department of General Medicine, D Y Patil University School of Medicine, Navi Mumbai

DOI:

https://doi.org/10.18203/2320-6012.ijrms20151472

Keywords:

Mixed connective tissue disease, CNS glioma, Vasculitis, Polymyositis

Abstract

Mixed connective tissue disease (MCTD) was first recognized by Sharp and Colleagues in 1972 among a group of patients with overlapping clinical features of systemic lupus erythematosis (SLE), scleroderma and myositis, with the presence of distinctive antibodies against, what now is known to be U1-ribonucleoprotein (RNP). We report an unusual case of a 23-year old female with MCTD characterized by the coexistence of signs, symptoms and immunological features of 3 defined autoimmune diseases SLE, systemic sclerosis (SSc), polymyositis (PM) and an unusual presence of central nervous system (CNS) Glioma.

References

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Published

2017-01-17

How to Cite

Parikh, R., Ingale, P., Dave, D., Pendse, M., Patil, S., & Bhate, A. (2017). A rare case of mixed connective tissue disease presenting with central nervous system glioma, vasculitis and polymyositis. International Journal of Research in Medical Sciences, 3(12), 3917–3920. https://doi.org/10.18203/2320-6012.ijrms20151472

Issue

Section

Case Reports