Eye of the tiger sign in neurodegeneration with brain iron accumulation: a case report
Keywords:
Neurodegeneration with brain iron accumulation, MRI, Eye of the tigerAbstract
Neurodegeneration with brain iron accumulation (NBIA) is a rare autosomal recessive disorder characterized by abnormal accumulation of ferritin in globus pallidus of brain. Magnetic resonance imaging (MRI) of brain demonstrates a characteristic ‘eye-of-the-tiger’ sign. We describe a case of NBIA in a child with classical clinical and MRI of brain features.
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