Eye of the tiger sign in neurodegeneration with brain iron accumulation: a case report

Authors

  • Sumantro Mondal Department of Medicine, R. G. Kar Medical College and Hospital, Kolkata, West Bengal
  • Debasish Dey Department of Radiology, Bangur Institute of Neurosciences, Kolkata, West Bengal
  • Tony Ete Department of Medicine, Institute of Post Graduate Medical Education and Research, Kolkata, West Bengal
  • Debanjali Sinha Department of Medicine, Institute of Post Graduate Medical Education and Research, Kolkata, West Bengal
  • Arijit Nag Department of Medicine, Institute of Post Graduate Medical Education and Research, Kolkata, West Bengal
  • Atanu Chakraborty Department of Medicine, Institute of Post Graduate Medical Education and Research, Kolkata, West Bengal
  • Amod Prasad Department of Medicine, R. G. Kar Medical College and Hospital, Kolkata, West Bengal

Keywords:

Neurodegeneration with brain iron accumulation, MRI, Eye of the tiger

Abstract

Neurodegeneration with brain iron accumulation (NBIA) is a rare autosomal recessive disorder characterized by abnormal accumulation of ferritin in globus pallidus of brain. Magnetic resonance imaging (MRI) of brain demonstrates a characteristic ‘eye-of-the-tiger’ sign. We describe a case of NBIA in a child with classical clinical and MRI of brain features.

References

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Published

2017-01-20

How to Cite

Mondal, S., Dey, D., Ete, T., Sinha, D., Nag, A., Chakraborty, A., & Prasad, A. (2017). Eye of the tiger sign in neurodegeneration with brain iron accumulation: a case report. International Journal of Research in Medical Sciences, 2(1), 370–372. Retrieved from https://www.msjonline.org/index.php/ijrms/article/view/2154