Extremely large size VSD with pulmonary stenosis

J. Rajendra Kumar, T. Sanath Kumar

Abstract


Defect in the ventricular septum with obstruction to right ventricular outflow tract encompass a wide anatomic, physiological & clinical spectrum. Large ventricular septal defects occur with pulmonary stenosis that varies from mild to severe to complete (pulmonary atresia). Very large VSD (size 6.4cm, in our case) with severe PS is a rare CHD & without surgical correction only 10% patients can survive beyond 20 year of age. With the help of noninvasive investigation (echocardiography) we can diagnose CHD very easily.


Keywords


CHD, VSD, PS, TOF

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References


Bertranou EG, Blackstone EH, Hazelrig JB, Turner ME, Kirklin JW. Life expectancy without surgery in tetralogy of Fallot. Am J Cardiol 1978;42:458-66.

Bain GO. Tetralogy of fallot: survival to seventieth year; report of a case. AMA Arch Pathol 1954;58:176-9.

Perloff JK. Venticular septal defect with pulmonary stenosis. In: Perloff JK, Editor. The Clinical Recognition of Congenital Heart Disease. Perloff JK (Editor), 4th ed. Philadelphia: W. B. Saunders Company;1999:476-89.

Lima CO, Sahn DJ, Valdes-Cruz LM, Goldberg SJ, Barron JV, Allen HD, et al. Noninvasive prediction of transvalvular pressure gradient in patients with pulmonary stenosis by quantitative two-dimensional echocardiographic Doppler studies. Circulation 1983;67:866-71.

McGoon MD, Fulton RE, Davis GD, Ritter DG, Neill CA, White RI Jr. Systemic collateral and pulmonary artery stenosis in patients with congenital pulmonary valve atresia and ventricular septal defect. Circulation 1977;56:473-9.

Rao BN, Anderson RC, Edwards JE. Anatomic variations in the tetralogy of Fallot. Am Heart J 1971;81:361-71.