Idiopathic hypertrophic pachymeningitis

Authors

  • Abhilash K Associate Professor of Medicine, Sree Gokulam Medical College, Thiruvananthapuram-695011, Kerala
  • Minimol KL Assistant Professor of Surgery, Government Medical College, Thiruvananthapuram-695607, Kerala

Keywords:

Idiopathic, Pachymeningitis, Steroids

Abstract

Idiopathic hypertrophic pachymeningitis is a rare form of granulomatous meningitis. It is mainly a diagnosis by exclusion. Here we are presenting a case of a young female presented with multiple cranial nerve palsies who was diagnosed to have hypertrophic pachymeningitis with the help of MRI brain. All available investigations showed negative results and so possibility of Idiopathic Hypertrophic Pachymeningitis was considered. The patient responded well to steroid therapy.

References

Goyal M, Malik A, Mishra NK, Gaikwad SB. Idiopathic hypertrophic pachymeningitis: spectrum of the disease. Neuroradiology 1997;39:619–623.

Mamelak AN, Kelly WM, Davis RL, Rosenblum ML. Idiopathic hypertrophic cranial pachymeningitis, report of three cases. J Neurosurg 1993;79:270–276.

Riku S, Kato S. Idiopathic hypertrophic pachymeningitis. Neuropathology. 2003;23:335–44.

Lindstorm KM, Cousar JB, Lopes MB. IgG4-related meningeal disease: clinico-pathological features and proposal for diagnostic criteria. Acta Neuropathol. 2010 Dec;120(6):765-76.

Downloads

Published

2017-01-28

How to Cite

K, A., & KL, M. (2017). Idiopathic hypertrophic pachymeningitis. International Journal of Research in Medical Sciences, 1(4), 599–600. Retrieved from https://www.msjonline.org/index.php/ijrms/article/view/2682