DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20171887

Dysembryoplastic neuropithelial tumor: a rare case report

Shailesh Thanvi, Hemant Jangid, Yogi Raj Joshi

Abstract


Dysembryoplastic neuropithelial tumor (DNET) is a rare recently described, benign glioneural tumor frequently associated with intractable seizures in children and young adults which is important to recognise clinically and radiologically as it is surgically curable without need for adjuvant chemoradiotherapy. We hereby present a case report of a 10year old male child who presented with intractable seizures and right parietal space occupying lesion which was diagnosed DNET radiologically, treated by microsurgical excision and confirmed histopathologically as DNET, thus emphasising multidisciplinary role in management of this rare entity.


Keywords


DNET, Epilepsy, Histopathology, MRI

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References


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