DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20174973

Surgical approach of bentall procedure in a patient of pectus excavatum

Subrata Pramanik, Ajit Padhy, Nayem Raja, Subodh Satyarthy

Abstract


A middle-aged man diagnosed case of Marfan syndrome associated with pectus excavatum presented with chest pain and dyspnea. Chest X-ray, transthoracic echocardiography and Computed tomography (CT) of heart and aorta revealed severe Aortic regurgitation with dilated aortic root, sinotubular junction and ascending aorta with normal size arch and descending aorta. Patient was taken for surgery. Pectus excavatum creates difficulties for heart exposure and cannulation for cardiopulmonary bypass. We planned for femoro-femoral bypass to carry out ahesiolysis and Bentall procedure without much difficulties. Postoperative stay of the patient was uneventful and followed up in regular interval.


Keywords


Ascending aorta, Bentall procedure, Cardiopulmonary bypass, Marfan syndrome, Pectus excavatum

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