Profile of arrythmogenic right ventricular cardiomyopathy/dysplasia (ARCV/D) patients presenting with sustained ventricular tachycardia in a tertiary care center

Authors

  • Rahul Sudan Department of General Medicine, Shri Guru Ram Rai Institute of Medical and Health Sciences, Shri Mahant Indresh Hospital (SGRRIMHS, SMI Hospital), Dehradun, Uttrakhand, India
  • Irfan Yaqoob Department of Cardiology, Sher I Kashmir Institute of Medical Sciences (SKIMS), Srinagar, Jammu and Kashmir, India
  • Khursheed Aslam Department of Cardiology, Sher I Kashmir Institute of Medical Sciences (SKIMS), Srinagar, Jammu and Kashmir, India
  • Mehroz Ahmad Department of General Medicine, Shri Guru Ram Rai Institute of Medical and Health Sciences, Shri Mahant Indresh Hospital (SGRRIMHS, SMI Hospital), Dehradun, Uttrakhand, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20181270

Keywords:

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D), Intracardiac defibrillator (ICD), Right ventricle (RV), Sustained ventricular tachycardia (VT), Sudden cardiac death (SCD)

Abstract

Background: Arrhythmogenic right ventricular cardiomyopathy /dysplasia (ARVC/D) is a genetic form of cardiomyopathy and is one among the most common causes of sudden cardiac death (SCD). The aim of our study was to analyze the clinical profile of (ARVC/D) patients presenting with sustained Ventricular Tachycardia (VT).

Methods: This single center cohort study evaluated 107 patients who presented with sustained ventricular tachycardia (VT) in our hospital. After aetiological evaluation of all these patients, 15 patients were found to have ARVC/D as the cause of sustained ventricular tachycardia (VT) as per the Modified Task Force Criteria. The clinical profile of these patients was observed in detail to enhance our knowledge about this entity in our part of the world.

Results: Mean age at presentation was 30 years and 12 patients were males. Nine patients were haemodynamically stable at the time of sustained VT and the rest of patients were haemodynamically unstable. Left Bundle Branch Block (LBBB) was the most common ECG morphology present in 11 patients. Antiarrhythmic drugs terminated VT in 7 patients. All the 6 patients presenting in a state of haemodynamic instability received DC cardioversion. Mortality occurred in 2 patients during the hospital stay.

Conclusions: ARVC/D presenting with sustained VT is an important manifestation of the disease. Males are more commonly affected than females. Haemodynamic instability at the time of presentation carries a poor prognosis.

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Published

2018-03-28

How to Cite

Sudan, R., Yaqoob, I., Aslam, K., & Ahmad, M. (2018). Profile of arrythmogenic right ventricular cardiomyopathy/dysplasia (ARCV/D) patients presenting with sustained ventricular tachycardia in a tertiary care center. International Journal of Research in Medical Sciences, 6(4), 1211–1216. https://doi.org/10.18203/2320-6012.ijrms20181270

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Original Research Articles