Dunbar syndrome: a rare presentation of abdominal angina treated by revascularization of the celiac artery by endovascular stenting

Rakshith Shetty; K. Subramanyam; Chinthu Sara Jacob

doi:10.18203/2320-6012.ijrms20182308

Authors

Rakshith Shetty Department of General Medicine, K. S. Hegde Medical Academy, Mangalore, Karnataka, India
K. Subramanyam Department of General Cardiology, K. S. Hegde Medical Academy, Mangalore, Karnataka, India
Chinthu Sara Jacob Department of General Medicine, K. S. Hegde Medical Academy, Mangalore, Karnataka, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20182308

Keywords:

Celiac artery compression syndrome, Celiac axis syndrome, Dunbar syndrome, Median arcuate ligament syndrome

Abstract

Median arcuate ligament syndrome (MALS) is a rare entity characterized by extrinsic compression of the celiac artery and symptoms of postprandial epigastric pain, nausea, vomiting, and weight loss mimicking mesenteric ischemia. The following case illustrates a rare cause of abdominal pain, where this young woman was found to have celiac trunk stenosis , secondary to compression of the trunk by the median arcuate ligament. She underwent a successful stenting to the ostial celiac trunk, thus reliving her symptomatically. Decompression of the celiac artery is the general approach. Usually post PTA, once revascularisation is achieved, 75% of the patients remain asymptomatic at follow up.

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