DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20182308

Dunbar syndrome: a rare presentation of abdominal angina treated by revascularization of the celiac artery by endovascular stenting

Rakshith Shetty, K. Subramanyam, Chinthu Sara Jacob

Abstract


Median arcuate ligament syndrome (MALS) is a rare entity characterized by extrinsic compression of the celiac artery and symptoms of postprandial epigastric pain, nausea, vomiting, and weight loss mimicking mesenteric ischemia. The following case illustrates a rare cause of abdominal pain, where this young woman was found to have celiac trunk stenosis , secondary to compression of the trunk by the median arcuate ligament. She underwent a successful stenting to the ostial celiac trunk, thus reliving her symptomatically. Decompression of the celiac artery is the general approach. Usually post PTA, once revascularisation is achieved, 75% of the patients remain asymptomatic at follow up.


Keywords


Celiac artery compression syndrome, Celiac axis syndrome, Dunbar syndrome, Median arcuate ligament syndrome

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References


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