Congenital cerebriform intradermal nevus presenting as cutis verticis gyrata: a case report

Ashish Jawarkar; Bhumika J. Gharia; Amrish N. Shah

doi:10.18203/2320-6012.ijrms20184063

Authors

Ashish Jawarkar Department of Pathology, Parul Institute of Medical Sciences and research, Vadodara, Gujarat, India
Bhumika J. Gharia Department of Pathology, Parul Institute of Medical Sciences and research, Vadodara, Gujarat, India
Amrish N. Shah Department of Pathology, Parul Institute of Medical Sciences and research, Vadodara, Gujarat, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20184063

Keywords:

Bull dog scalp, Cerebriform intradermal nevus, Cutis verticis gyrata

Abstract

Cerebriform intradermal nevus is a rare disorder characterised by development of folds and furrows on the scalp, giving it a convoluted appearance resembling surface of the brain. There are two main forms of CVG, primary and secondary. Secondary form may appear at any age and is usually secondary to causes such as tumors, Cerebriform intradermal nevus (CIN), neurofibromas or amyloidosis. There is high risk of development of malignant melanoma in patients of CIN presenting as CVG. Hence early diagnosis and treatment is important.

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