DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20184063

Congenital cerebriform intradermal nevus presenting as cutis verticis gyrata: a case report

Ashish Jawarkar, Bhumika J. Gharia, Amrish N. Shah

Abstract


Cerebriform intradermal nevus is a rare disorder characterised by development of folds and furrows on the scalp, giving it a convoluted appearance resembling surface of the brain. There are two main forms of CVG, primary and secondary. Secondary form may appear at any age and is usually secondary to causes such as tumors, Cerebriform intradermal nevus (CIN), neurofibromas or amyloidosis. There is high risk of development of malignant melanoma in patients of CIN presenting as CVG. Hence early diagnosis and treatment is important.


Keywords


Bull dog scalp, Cerebriform intradermal nevus, Cutis verticis gyrata

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References


Tabata H, Yamakage A, Yamazaki S. Cerebriform intradermal nevus. Int J Dermatol. 1995;34:634.

Van Geest AJ, Berretty PJ, Klinkhamer PJ, Neumann HA. Cerebriform intradermal naevus (a rare form of secondary cutis verticis gyrata) J Eur Acad Dermatol Venereol. 2002;16:529-31.

Tagore KR, Ramineni AS. A case of cutis verticis gyrata secondary to giant cerebriform intradermal nevus. Indian J Pathol Microbiol. 2011;54:624-5.

Keen MA, Hassan I. A case of cutis verticis gyrata associated with epilepsy. J Pakistan Association Dermatol. 2014;24(2):186-8.

Schenato LK, Gil T, Carvalho LA, Ricachnevsky N, Sanseverino A, Halpern R. Essential primary cutis verticis gyrata. J Pediatria. 2002 Feb;78(1):75-80.

Phiske M. Cerebriform intradermal nevus: A rare entity and its associations. Indian Dermatology Online J. 2014;5(2):115-6.

Yazici AC, Ikizoglu G, Baz K, Polat A, Ustunsoy D. Cerebriform intradermal nevus. Pediatr Dermatol. 2007;24:141-3.