Published: 2016-12-25

A rare case of lutembacher syndrome in a young female: a case report from a rural population of Western Uttar Pradesh, India

Priyesh Kant, Prem Shanker Singh, Khwaja Saifullah Zafar, Himanshu Sharma


Lutembacher syndrome is a rare entity presenting with a combination of congenital atrial septal defect with acquired mitral stenosis. Lutembacher syndrome is reported to be more prevalent in developing countries where the incidence of rheumatic fever is high. We also came across with a young female with the similar clinical presentation in our hospital situated in a rural area in Western Uttar Pradesh, India. Keeping in mind its rare occurrence, we are presenting an overview of this syndrome including its various aspects and the problems faced by the patients in rural scenario. 


Lutembacher syndrome, Mitral stenosis, atrial septal defect, Rural population

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