DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20192928

Ross syndrome: a case report

Manoj Kr. Mahata, Saikat Ghosh, K. C. Ghosh, R. Bhattacharyya, G. P. Mondal

Abstract


Ross syndrome is a rare partial dysautonomic syndrome of unknown aetiology, characterized by segmental hypo/ anhidrosis associated with Holmes-Adie syndrome (tonic pupil and hypo/areflexia). The hypohydrosis or anhydrosis is patchy initially, later it becomes segmental or diffuse. This is due to affection of postganglionic cholinergic parasympathetic and sympathetic fibers involvement. There are a very few cases (approximately 50) have been reported in the literature since its original description. Author report a 22 years old male with classical features of Ross syndrome.


Keywords


Anhidrosis, Areflexia, Ross syndrome

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References


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