Ross syndrome: a case report
DOI:
https://doi.org/10.18203/2320-6012.ijrms20192928Keywords:
Anhidrosis, Areflexia, Ross syndromeAbstract
Ross syndrome is a rare partial dysautonomic syndrome of unknown aetiology, characterized by segmental hypo/ anhidrosis associated with Holmes-Adie syndrome (tonic pupil and hypo/areflexia). The hypohydrosis or anhydrosis is patchy initially, later it becomes segmental or diffuse. This is due to affection of postganglionic cholinergic parasympathetic and sympathetic fibers involvement. There are a very few cases (approximately 50) have been reported in the literature since its original description. Author report a 22 years old male with classical features of Ross syndrome.
Metrics
References
Nolano M, Provitera V, Perretti A, Stancanelli A, Saltalamacchia AM, Donadio V, et al. Ross syndrome: a rare or a misknown disorder of thermoregulation? a skin innervation study on 12 subjects. Brain. 2006;129(8):2119-31.
Luong M, Jomir L, Labauge P, Dandurand M, Meunier L, Stoebner PE. Ross syndrome with sweating anomaly associated with Sjögren syndrome: an infrared thermo-graphic case study. Acta Derm Venereol. 2011;91(1):80-1.
Vasudevan B, Sawhney M, Vishal S. Ross syndrome with ana positivity: A clue to possible autoimmune origin and treatment with intravenous immunoglobulin. Indian J Dermatol. 2010;55(3):274-6.
Nolano M, Provitera V, Donadio V, Stancanelli A, Saltalamacchia A, Caporaso G, et al. Ross syndrome: a lesson from a monozygotic twin pair. Neurol. 2013;80(4):417-8.
Nagane Y, Utsugisawa K. Ross syndrome associated with cytomegalovirus infection. Muscle Nerve. 2008;38(1):924-6.
Sawhney MP, Sharma YK, Singh N. Segmental anhidrosis with hyporeflexia associated with congenital spinal deformity: a Ross's syndrome variant or inverse Horner's syndrome? Indian J Dermatol Venereol Leprol. 2004;70(1):29-32.
Shin RK, Galetta SL, Ting TY, Armstrong K, Bird SJ. Ross syndrome plus: beyond horner, Holmes-Adie, and harlequin. Neurology 2000;55:1841-6.
Diez BM, Rio GI, Dauden E, Arroyo CM, Diez GA. Ross syndrome, an entity included within the spectrum of partial disautonomic syndromes. J Eur Acad Dermatol Venereol. 2005;19(6):729-31.
Downloads
Published
How to Cite
Issue
Section
