DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20194195

Management mature sacrococcygeal teratoma: a case report

Budiman Ritonga, Kadek Deddy Ariyanta, I. Made Darmajaya

Abstract


Mature sacrococcygeal teratoma (SCT) are uncommon neoplasm comprised of mixed elements derived from three germ layers. They attract attention because of their gross appearance and bizarre histology. Tumor of the sacrococcygeal region, referred to as sacrococcygeal teratomas (SCTs) in most reports, generally present in two distinct fashions: neonates with large predominately external lesions, which are detected in utero or at birth and are rarely malignant; and older infants and children who present with primarily hidden pelvic tumors with a much higher rate of malignancy. Sacrococcygeal teratomas are the most common extragonadal tumor in neonates, accounting for up to 70% of all teratomas in childhood. A 3 to 4:1 female to male ratio is generally reported. Surgical resection remains the mainstay of therapy and recurrence is rare following complete excision. A 14 years old girl was presented to us by her parents with a mass at the buttock since birth. She was delivered at home by traditional midwife after a term, unsupervised pregnancy to a 35 years old woman. Both pregnancy and delivery were uneventful. Direct rectal examination revealed a mass has displaced the recto-sigmoid anteriorly. The CT scan revealed a heterogenous mass with a solid, cystic, and multiple classification density at the anterior of coccygeus bone, and push the coccygeus to the posterior. The mass infiltrated the subcutis, and attached to the posterior aspect of rectum. A 14 years old girl presented by mature SCT since newborn comprising ectoderm, mesoderm, and endoderm tissue. She had a complete surgical excision (including coccygectomy) with primary wound closure. A complete surgical excision remains the mainstay of therapy of mature SCT.


Keywords


Childhood, Neoplasm, Sacrococcygeal teratoma, Surgical excision

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References


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