Retroperitoneal lymphangiectasia: a great clinical masquerade


  • Siddhant Uttam Manwar Department of Radio-Diagnosis, B.Y.L. Nair Ch. Hospital and Topiwala National Medical College, Mumbai, Maharashtra, India
  • Manisha Vishnu Joshi Department of Radio-Diagnosis, Topiwala National Medical College, Mumbai, Maharashtra, India
  • Devdas Sudhakar Shetty Department of Radio-Diagnosis, Topiwala National Medical College, Mumbai, Maharashtra, India
  • Upendra Diwakar Bhalerao Department of Cardiovascular and Thoracic Surgery, Sir JJ Group of Hospitals and Grant Medical College, Mumbai, Maharashtra, India



Computed Tomography, Contrast enhanced Computed Tomography, Magnetic resonance imaging Retroperitoneal lymphangiectasis, Ultrasonography


Retroperitoneal lymphangiectasia is a very rare lymphatic disorder characterized by abnormal proliferation of lymphatics. We present series of 3 cases of retroperitoneal lymphangiectasia which are diagnosed in our institute with the help of Ultrasonography (USG), Computed Tomography (CT) and Magnetic resonance imaging (MRI) of abdomen and pelvis with unusual clinical presentation. We include clinical features and imaging findings of this disorder with its pathogenesis and diagnosis. Two of the cases were clinically masquerading as hernia and one case was mimicking varicocele. Thorough clinical examination and USG, colour Doppler, CT and MRI are extremely helpful imaging investigation that aid in differentiating these lesions from hernia/ varicocele and the cross sectional imaging like CT and MRI can  depict the anatomical extent of the disease.


Kosir MA, Sonnino RE, Gauderer MWL. Pediatric abdominal lymphangiomas: a plea for early recognition. J Pediatr Surg.1991;26(11):1309-13.

Jackson IT, Carreño R, Potparic Z, Hussain K. Hemangiomas, vascular malformations, and lymphovenous malformations: classification and methods of treatment. Plast Reconstr Surg. 1993;91(07):1216-30.

Joshua A, Cox, Bartlett E, Lee EI. Vascular Malformations: A Review. Semin Plast Surg. 2014 May;28(2):58-63.

Davidson AJ, Hartman DS. Lymphangioma of the retroperitoneum. CT and sonographic characteristics. Radiol. 1990;175:507-10.

Ko SF, Ng SH, Shieh CS, Lin JW, Huang CC, Lee TY. Mesenteric cystic lymphangioma with myxoid degeneration: unusual CT and MR manifestations. Pediatr Radiol. 1995;25:525-7.

Moukaddam H, Pollak J, Haims AH. MRI characteristics and classification of peripheral vascular malformations and tumors. Skeletal Radiol. 2009;38(6):535-47.

Donnelly LF, Adams DM, Bisset GS. Vascular malformations and hemangiomas: a practical approach in a multidisciplinary clinic. AJR Am J Roentgenol. 2000;174(3):597-608.

Kajal P, Rattan KN, Malik VS, Garsa V. Scrotal Lymphangioma–a rare cause of scrotal swelling. APSP J Case Reports. 2013 Jan;4(1):5.




How to Cite

Manwar, S. U., Joshi, M. V., Shetty, D. S., & Bhalerao, U. D. (2020). Retroperitoneal lymphangiectasia: a great clinical masquerade. International Journal of Research in Medical Sciences, 8(2), 748–753.



Case Reports