Retroperitoneal lymphangiectasia: a great clinical masquerade

Siddhant Uttam Manwar; Manisha Vishnu Joshi; Devdas Sudhakar Shetty; Upendra Diwakar Bhalerao

doi:10.18203/2320-6012.ijrms20200267

Authors

Siddhant Uttam Manwar Department of Radio-Diagnosis, B.Y.L. Nair Ch. Hospital and Topiwala National Medical College, Mumbai, Maharashtra, India
Manisha Vishnu Joshi Department of Radio-Diagnosis, Topiwala National Medical College, Mumbai, Maharashtra, India
Devdas Sudhakar Shetty Department of Radio-Diagnosis, Topiwala National Medical College, Mumbai, Maharashtra, India
Upendra Diwakar Bhalerao Department of Cardiovascular and Thoracic Surgery, Sir JJ Group of Hospitals and Grant Medical College, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20200267

Keywords:

Computed Tomography, Contrast enhanced Computed Tomography, Magnetic resonance imaging Retroperitoneal lymphangiectasis, Ultrasonography

Abstract

Retroperitoneal lymphangiectasia is a very rare lymphatic disorder characterized by abnormal proliferation of lymphatics. We present series of 3 cases of retroperitoneal lymphangiectasia which are diagnosed in our institute with the help of Ultrasonography (USG), Computed Tomography (CT) and Magnetic resonance imaging (MRI) of abdomen and pelvis with unusual clinical presentation. We include clinical features and imaging findings of this disorder with its pathogenesis and diagnosis. Two of the cases were clinically masquerading as hernia and one case was mimicking varicocele. Thorough clinical examination and USG, colour Doppler, CT and MRI are extremely helpful imaging investigation that aid in differentiating these lesions from hernia/ varicocele and the cross sectional imaging like CT and MRI can depict the anatomical extent of the disease.

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