Huriez syndrome: a rare palmoplantar keratoderma

Ajay Kumar, Geeta Ram Tegta, Ghanshyam Kumar Verma


The Huriez syndrome is a rare autosomal dominant transgradient palmoplantar keratoderma which is characterized by scleroatrophy of the fingers, nail changes and squamous cell carcinomas in affected skin. Herein, we present a non-familial case of very rare plamoplantar keratoderma with scleroatrophy - the Huriez syndrome in a 45 year old female patient.


Palmoplantar keratoderma, Transgredient, Autosomal dominant

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